Abstract:
Introduction: Primary urethral carcinoma is a rare disease with overall poorer outcomes in the past. It is relatively
more uncommon in female sex.
Clinical presentation: We present a case of a female with primary urethral carcinoma that presented atypically as a
vulval mass without any features of storage, voiding lower urinary tract symptoms, or gross haematuria.
Discussion: As primary urethral carcinoma is rare in occurrence, prospective studies are limited so as the rec-
ommendations to guide treatment options. Treatment recommendations are still on development from different
small-scale studies as well as from data in higher volume centers. Management options depends on location,
extent, histology of the lesion as well as on sex of the patient and fitness of the patient.
Conclusion: Early diagnosis and treatment with multidisciplinary consult and multimodality will improve the
overall survival rate and quality of life of the patients.
